재발성 뇌막염을 동반한 Mondini Dysplasia 치험 1례

In children, recurrent meningitis occuring independent to a systemic bacterial infection should be considered as a result of cerebrospinal fluid(CSF) leak due to inner ear anormaly.

Mondini dysplasia is the most commonly encountered inner ear deformity causing CSF leak with hearing impairment.

In many cases, that may have residual hearing and so the hearing can be preserved or improved by use of hearing aid or cochlear implant, but when it is associated with CSF leak, age and recurrent meningitis though hearing preservation is ideal, the primary goal of treatment must be to stop and lose the CSF leak.