Journal of Clinical Otolaryngology Head and Neck Surgery

The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery

J Clin Otolaryngol Head Neck Surg 1995; 6(1):77-82

pISSN: 1225-0244, eISSN: 2713-833X

DOI: https://doi.org/10.35420/jcohns.1995.6.1.77

임상

재발성 뇌막염을 동반한 Mondini Dysplasia 치험 1례

서한규¹, 박호정¹, 김혜정¹, 황순재¹

A Case of Mondini Dysplasia with Recurrent Meningitis

Han Kyu Shu¹, Hye Jeong Kim¹, Ho Jeong Park¹, Soon Jae Hwang¹

¹고려대학교 의과대학 이비인후·두경부외과학 교실

¹Department of Otolaryngology-Head and Neck Surgery Collage of Medicine, Korea University

© Copyright 1995 The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery. This is an Open-Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Published Online: May 31, 2020

ABSTRACT

In children, recurrent meningitis occuring independent to a systemic bacterial infection should be considered as a result of cerebrospinal fluid(CSF) leak due to inner ear anormaly.

Mondini dysplasia is the most commonly encountered inner ear deformity causing CSF leak with hearing impairment.

In many cases, that may have residual hearing and so the hearing can be preserved or improved by use of hearing aid or cochlear implant, but when it is associated with CSF leak, age and recurrent meningitis though hearing preservation is ideal, the primary goal of treatment must be to stop and lose the CSF leak.

Keywords: Recurrent meningitis; CSF leak; Mondini dysplasia