소뇌교각의 악성 림프종 : 돌발성 난청의 드문 원인 1예

Cerebellopontine angle (CPA) tumor is a rare cause of sudden deafness, with the probability of 0.8-4.0%, and mostly acoustic neurinoma. Autoimmune inflammatory rheumatic diseases can increase the risk of malignant lymphoma. As a consequence of increasing life expectancy of immune-mediated disease patients and growing prevalence of those disease among average population, the incidence of malignant lymphoma is expected to increase. However, central nervous system (CNS) lymphoma either primary or secondary is very rare moreover when locating in the CPA. Therefore, it is very difficult to speculate malignant lymphoma in sudden deafness. We present a rare case that 45-year-old man, who has taken immunosuppressant for systemic lupus erythematosus and systemic sclerosis suffered sudden hearing loss in his right ear due to CPA malignant lymphoma. (J Clinical Otolaryngol 2016;27:316-321)