우측 외이도에 발생한 제1형 신경섬유종증 1례

Neurofibromatosis is a group of related genetic disorder of neuroectodermal tissue characterized by CNS, PNS tumors and disorders, cafe-au-lait spots, generalized cutaneous neurofibromata, skeletal deformities and endocrine abnormalities. It involves in head and neck area about 25-30%. In 1987, according to genetics, National Institute of Health clarified the two main types of neurofibroma. Recently, the authors experienced a case of neurofibromatosis type I on right external auditory canal and treated with surgery and pathologic diagnosis was benign neurofibroma. (J Clinical Otolaryngol 2000;11:304-308)