즉두골에 발생한 섬유성 이형성증 1례

Fibrous dysplasia is a relatively rare condition characterized by fibrous tissue replacement of skeleton. The etiology is unkonwn, but it is now believe to be a developmental error in which primitive fibrous tissue proliferates within the bony medulla and enchroaches up on the cortex. Fibrous dysplasia of the temporal bone is an extremely rare disease in otologic field. Two forms of fibrous dysplasia are recognized: monostotic form and polyostotic multifocal form. Monostotic fibrous dysplasia, an unusual disease that can involve the temporal bone, will frequently cause an acquired stenosis of the external auditory canal and develope external canal cholesteatoma.

Authors experienced a case of fibrous dysplasia of temporal bone in 42 years old male, and reported this case with brief review of literatures.