증례

즉두골에 발생한 섬유성 이형성증 1례

엄준형1, 정운교1, 박상일1, 박미향1
Jun Hyung Eum1, Woon Kyo Chung1, Sang II Park1, Mi Hyang Park1
Author Information & Copyright
1이화여자대학교 이비인후과학교실
1Department of Otolaryngology, College of Medicine, Ewha Womans University, Seoul, Korea

© Copyright 1996 The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery. This is an Open-Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Published Online: May 31, 2020

ABSTRACT

Fibrous dysplasia is a relatively rare condition characterized by fibrous tissue replacement of skeleton. The etiology is unkonwn, but it is now believe to be a developmental error in which primitive fibrous tissue proliferates within the bony medulla and enchroaches up on the cortex. Fibrous dysplasia of the temporal bone is an extremely rare disease in otologic field. Two forms of fibrous dysplasia are recognized: monostotic form and polyostotic multifocal form. Monostotic fibrous dysplasia, an unusual disease that can involve the temporal bone, will frequently cause an acquired stenosis of the external auditory canal and develope external canal cholesteatoma.

Authors experienced a case of fibrous dysplasia of temporal bone in 42 years old male, and reported this case with brief review of literatures.

Keywords: Fibrous dysplasia; Temporal bone