외이기형을 동반하지 않은 선천성 이소골 기형 2례

Congenital ossicular anomalies, one of the causes of congenital hearing loss, may occur without deformity of the external ear. We experienced 3 cases of congenital conductive hearing loss due to ossicular anomalies confirmed by exploratory tympanotomy. A 6-year-old girl presented with bilateral hearing loss which had been present since youth. At tympanotomy, the long process of the incus was absent in each ear. A PORP prosthesis was replaced between head of stapes and ear drum. The hearing showed improvement. A 27-year- old male presented with right hearing loss since childhood, the long process of the incus and stapes was absent. A TORP prosthesis was used. The hearing was improved.

Authors report 3 ears of congenital ossicular anomaly without deformity of external ear. Ossiculoplasty was done by use of PORP or TORP with favorable postoperative results.