후두개와 및 중두개와 침범을 동반한 거대한 선천성 진주종 1례

Congenital cholesteatomas histologically are epidermoid tumors originating from embroynic epidermoid rests located anywhere in the temporal bone or adjacent epidural and meningeal spaces. Mostly they occur in the temporal bone, and epidural or meningeal cholesteatomas are very rare. The clinical symptoms depend upon the site and the size of the lesion.

Recently authors have experienced one case of huge cholesteatoma with posterior and middle cranial fossa extension. The tumor was removed successively by craniotomy through infratemporal dissection. We report it with review of literatures.