심장 및 신장기형을 가진 환아에서 선천성 진주종으로 오인된 중이강 내 침샘 분리종 1예

A choristoma is a nonneoplastic proliferation of histologically normal tissue that forms at an abnormal site. Salivary gland choristoma of the middle ear cavity is extremely uncommon. It is thought to be a developmental abnormality and may be associated with abnormalities of adjacent structures. It usually requires a differential diagnosis from other mass lesions in the middle ear cavity. We report a case of salivary gland choristoma of the middle ear suspected as congenital cholesteatoma in a 6-year-old girl with cardiac and renal malformations with a review of the literature. This patient is the first reported case combined with other abnormalities in Korea. (J Clinical Otolaryngol 2011;22:94–97)