악하선관 결석 환자에서 발견된 일측성 악하선 무형성 1예

The congenital absence of major salivary glands is an extremely rare disorder. The cause of congenital absence of the salivary glands has not been determined, but it may be associated with ectodermal defects of the first and second branchial arches. The etiopathogenesis of isolated absence of a major salivary gland without other developmental anomalies is still unclear. Unilateral aplasia of the submanibular gland with sialolithiasis of contralateral wharton’s duct has not been reported previously. The authors report with relative literature one case of Unilateral aplasia of the submanibular gland with sialolithiasis of contralateral Wharton’s duct. (J Clinical Otolaryngol 2010;21:279-282)