돌발성 난청을 주소로 내원한 제2형 신경섬유종증환자의 방사선 치료 후 청력개선 1예

Neurofibromatosis type II is an autosomal dominant disorder that predisposes affected individuals to the development of bilateral vestibular schwannomas. The course of hearing loss is particularly important because, with bilateral involvement, the patient will eventually become deaf, and other disabilities. Clinical management trys to minimize and delay this morbidity. It has been controversial to determine to wait and see or to try surgical management for hearing preservation. Especially, decision making in patients with a vestibular schwannoma in the only hearing ear is challenging. We experienced a case of sudden hearing loss with a nerofibromatosis type II patient in the only hearing ear. His vestibular schwannomas were treated with stereotactic radiosurgery (gamma-knife) with hearing restoration. (J Clinical Otolaryngol 2007;18:261–265)