한국 Turner 증후군 환자에서의 이과적 발현

Background and Objectives:Patients with Turner’s syndrome have been frequently suspected to have associated otologic disorders and hearing loss. The purpose of this study was to elucidate the otologic problems in Turner’s Syndrome Patients, such as incidence, degree, and types of hearing loss. Patients and Methods:The 12 subjects aged 5 and 30 years who were previous diagnosed with Turner’s syndrome were investigated for the otologic manifestations. All the patients were evaluated audiologically. Results:Clinical examination revealed the his-tories of otitis media in 3 subjects (25%). A audiological examination were performed for all subjects and revealed normal hearing in 8 subjects (62%), unilateral hearing loss in 2 subjects (17%), bilateral hearing loss in 2 subjects (17%). Type of the hearing loss was conductive type in 2 ears (8%), mixed type in 2 ears (8%), sensorineural type in 2 ears (8%). Degree of hearing loss was mild in 5 ears, moderate in 1 ear. Conclusion:Our results demonstrated that the otitis media and hearing loss were common for Turner’s syndrome patients. The findings emphasize the importance of regular otological examinations and audiological evaluation of all girls with Turner’s syndrome early in life. (J Clinical Otolaryngol 2005;16:41–44)