일측성 말초 전정계를 침범한 신경베체트병 치험 1예

Behçet’s disease is a chronic, multisystemic disorder that affects mainly young adults and is characterized by a relapsing inflammatory process of unknown cause. It was originally described as a clinical triad of oral aphthae, genital ulcers, ocular lesions. Furthermore, cutaneous, central nervous system, vascular and cardiovascular, gastointestinal, renal, and pleuropulmonary lesions, arthritis, and epididymitis are today accepted as additional clinical features of Behçet’s syndrome. Hearing loss and dizziness are frequent symptoms in patients affected by Behçet’s syndrome with or without the involvement of the CNS. Peripheral involvement is more common than central involvement for vestibulocochlear lesions. In addition, vestibular deficit may represent an early sign of neuro-Behçet’s syndrome (CNS lesion in behçet’s disease). We experienced unilateral peripheral vestibular involvement without cochlear involovement in neuro-Behçet’s syndrome, so we report this case with a review of literature. (J Clinical Otolaryngol 2005;16:140-143)