접형동과 사골동에 발생한 단골성 섬유이형성증 1례

Fibrous dysplasia is a benign, chronic, slowly progressive bone disorder of unknown etiology characterized by replacement of normal bone by a variable amount of fibrous tissue and woven bone. The proportions of the fibrous tissue and osseous tissue vary occasionally even in the same bone. Depending on one or more bones affected, monostotic and polyostotic forms were defined and in a small percentage of cases the polyostotic form is associated with endocrine disturbances, such as McCune-Albright syndrome. Because the fibrous dysplasia has predilection for membranous bone such as femur and tibia, it’s origin in the enchondral bone such as sphenoid sinus and ethmoid sinuses is very rare. Recently we experienced a case of monostotic fibrous dysplasia of sphenoid and ethmoid sinuses. So the case will be discussed with literature review. (J Clinical Otolaryngol 2003;14:144-147)