증례

측두골에 발생한 섬유성 이형성증 1례

채세용1,*, 노혜일1, 이종우1, 류재영1, 정은선2
Sayong Chae1,*, Heil Noh1, Jong Woo Lee1, Jae Joung Ryu1, Eun Sun Jeong2
Author Information & Copyright
1가톨릭대학교 의과대학 이비인후과교실
2임상병리학교실
1Department of Otolaryngology Head and Neck Surgery, The Catholic University of Korea, Seoul, Korea
2Clinical Pathology, College of Medicine, The Catholic University of Korea, Seoul, Korea
*교신저자: 노혜일, 442-060 경기도 수원시 팔달구 지동 93 번지 가톨릭대학교 의과대학 이비인후과학교실 전화: (031) 249-7450· 전송: (031)257-3752 E-mail: nhi1@unitel.co.kr

© Copyright 2000 The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery. This is an Open-Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Received: Oct 09, 1999; Accepted: Feb 12, 2000

Published Online: May 31, 2020

ABSTRACT

Fibrous dysplasia is a bone disorder of unknown etiology in which normal bone is replaced with fibrotic tissue and disorganized immature bone trabeculae. The disease has three variants ; monostotic, polyostotic, and Al- brighfs syndrome. Monostotic fibrous dysplasia especially involving mainly squama in temporal bone is rare. The clinical course of them is unpredictable. Monostotic form arises usually in childhood and often come to an arrest at puberty. Polyostotic form without endocrine dysfunction tends to appear at a slightly earlier age than the monostotic form and may progress into middle age. Mostly their involvement is unilateral. Monostotic form involving temporal bone is associated with conductive hearing loss attributable to compression of the external auditory canal. Potential problems include cholesteatoma, recurrence and malignant transformation. We report a case of monostotic fibrous dysplasia of temporal bone involving mainly squama, which is succe-ssfully treated with canaloplasty and skin graft. We also observed the eletron microscopic findings. (J Clinical Otolaryngol 2000;11:109–114)

Keywords: 섬유성 이형성증; 측두골; 인상부; 전자현미경
Keywords: Fibrous dysplasia; Temporal bone; Squama; Electron microscopy