Journal of Clinical Otolaryngology Head and Neck Surgery
The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery
증례

어지럼증을 주소로 내원한 아놀드 키아리 기형 1예

장연일1, 유한석1, 정재호1, 이승환1,*
Youn Il Jang1, Han Seok You1, Jae Ho Chung1, Seung Hwan Lee1,*
1한양대학교 의과대학 이비인후-두경부외과학교실
1Department of Otorhinolaryngology-Head and Neck Surgery, Hanyang University College of Medicine, Seoul, Korea
*교신저자: 이승환, 04763 서울 성동구 왕십리로 222 한양대학교 의과대학 이비인후-두경부외과학교실 전화: (031) 560-2368·전송:(031) 566-4884 E-mail:Shleemd@hanyang.ac.kr

© Copyright 2017 The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery. This is an Open-Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Received: Oct 05, 2016; Revised: Feb 02, 2017; Accepted: Mar 15, 2017

Published Online: May 31, 2020

ABSTRACT

A type 1 Arnold-Chiari malformation is defined by herniation of cerebellar tonsil through the foramen magnum. It is usually asymptomatic until three decades to five decades. Symptoms of type 1 Arnold-Chiari malformation are headache, lower cranial palsy, motor weakness and ataxia. However, isolated vertigo has rarely been described as a first presenting symptom of the disease. A seven-year-old boy presented with acute vertigo. A left beating horizontal nystagmus was identified, while the caloric response was normal. And other neurologic deficits were not evident. Magnetic resonance image confirmed a type 1 Arnold-Chiari malformation and decompressive surgery has been performed. After surgery, nystagmus was disappeared and subjective dizziness was improved. An isolated vertigo might be a first symptom of type 1 Arnold-Chiari malformation. We must consider the possibility of congenital malformation in the differential diagnosis of vertigo. (J Clinical Otolaryngol 2017;28:81-85)

Keywords: 아놀드 키아리 기형; 현훈
Keywords: Arnold chiari malformation; Vertigo