Table 4. Frequency-specific air-conduction thresholds in 5 children who underwent pure-tone audiometry

Case	Gene	Age (yr)	Ear	125	250	500	1k	2k	3k	4k	8k	6FA
1	GJB2	7.8	R	15	10	15	10	10	10	5	5	10.0
			L	10	10	5	10	5	5	5	5	6.7
2	SLC26A4	6.7	R	15	10	15	15	15	10	10	5	14.2
			L	5	5	5	10	10	10	10	5	9.2
3	MT-RNR1	7.4	R	10	10	5	10	5	5	5	15	6.7
			L	10	5	5	5	5	0	10	0	5.8
4	MT-RNR1	5.0	R	10	10	10	10	5	10	10	10	8.3
			L	10	10	10	5	5	10	5	5	5.8
5	SLC26A4	4.5	R	10	10	10	15	10	10	5	15	10.8
			L	10	10	10	10	15	10	15	10	12.5

Values are presented in dB HL; column headings indicate stimulus frequency in Hz (k=1,000 Hz).
Age: age at pure-tone audiometry, R: right ear, L: left ear, 6FA: six-frequency average (500+2×1,000+2×2,000+4,000 Hz)/6.