Table 1. Sinonasal neuroendocrine tumor grade 1 and 2 (well-differentiated and moderately differentiated neuroendocrine carcinomas; typical carcinoid and atypical carcinoid): review of published cases

Author Patient Age/sex Location Histopathological subtype Mitotic index Ki-67% Treatment Outcome Follow-up
Mhawej R18) 1 51/M NPX MD (AC) 1 3 OP NED 14 mo
Likhacheva A19) 2 22/M NS MD NS NS OP NED 166 mo
3 67/F NS MD NS NS OP, C, R DOD 56 mo
4 43/F NS MD NS NS OP, R NED 31 mo
5 46/F NS MD NS NS C, R NED 16 mo
6 54/M NS MD NS NS OP, C, R Nodal metastasis (46 mo), NED 107 mo
7 47/M NS MD NS NS OP, R Nodal metastasis (125 mo), NED 172 mo
8 54/M NS MD NS NS OP, C, R Local recurrence (80 mo), DOD 119 mo
Vandist V20) 9 48/M S, NPX WD (TC) <1 low C, R NS NS
Wang CP6) 10 67/F NC MD (AC) NS NS OP Local recurrence 14 mo
11 63/M NC MD (AC) NS NS OP, C, R NED 16 mo
12 42/F E WD (TC) NS NS OP NED 84 mo
Perez-OrdoƱez B21) 13 34/M S, NPX MD (AC) 2 NS C, R AWD 84 mo
Stephenson KA22) 14 48/M NC, S MD (AC) NS NS OP NED 36 mo
Lee DH17) 15 76/M NC WD (TC) NS NS OP NED 12 mo
Maharaj S12) 16 65/F NC, M, S MD 9 NS OP, R NED 93 mo
Kao HL11) 17 25/M NC MD 4 6 OP, C, R AWD 53 mo
18 59/M NC MD 7 17 OP NED 60 mo
19 41/M NC MD 8 18 OP NED 65 mo
20 24/F E MD 6 7 OP AWD 78 mo
21 31/M NC MD 6 6 OP NED 50 mo
22 23/M NC WD 0 1 OP NED 42 mo
Current report 23 46/M NC MD (AC) 8 3 to 4 OP NED 36 mo
NPX: nasopharynx, M: maxillary sinus, E: ethmoid sinus, S: sphenoid sinus, NC: nasal cavity, NS: not specified, WD: well-differentiated, MD: moderately differentiated, TC: typical carcinoid, AC: atypical carcinoid, OP: operation, C: chemotherapy, R: radiotherapy, NED: no evidence of disease, DOD: died of disease, AWD: alive with disease, mo: months.